{"id":18439,"date":"2022-05-16T17:29:25","date_gmt":"2022-05-16T15:29:25","guid":{"rendered":"https:\/\/staging.metax.org\/single-amino-acids\/"},"modified":"2025-12-23T09:41:18","modified_gmt":"2025-12-23T08:41:18","slug":"single-amino-acids","status":"publish","type":"page","link":"https:\/\/staging.metax.org\/en\/single-amino-acids\/","title":{"rendered":"Single Amino Acids"},"content":{"rendered":"<p><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-1 fusion-flex-container nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"--awb-border-sizes-top:0px;--awb-border-sizes-bottom:0px;--awb-border-sizes-left:0px;--awb-border-sizes-right:0px;--awb-border-color:var(--awb-custom_color_2);--awb-border-radius-top-left:0px;--awb-border-radius-top-right:0px;--awb-border-radius-bottom-right:0px;--awb-border-radius-bottom-left:0px;--awb-padding-top:0px;--awb-padding-right:0px;--awb-padding-bottom:0px;--awb-padding-left:0px;--awb-padding-top-medium:0px;--awb-margin-top:48px;--awb-margin-bottom:0px;--awb-margin-top-medium:0px;--awb-flex-wrap:wrap;\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-flex-start fusion-flex-align-content-flex-start fusion-flex-content-wrap\" style=\"max-width:1248px;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-0 fusion_builder_column_1_1 1_1 fusion-flex-column fusion-flex-align-self-flex-start\" style=\"--awb-padding-top:14px;--awb-padding-right-small:0px;--awb-bg-image:radial-gradient(circle at center center, var(--awb-color1) 0%,var(--awb-color4) 100%);--awb-bg-size:cover;--awb-width-large:100%;--awb-margin-top-large:0px;--awb-spacing-right-large:1.92%;--awb-margin-bottom-large:0px;--awb-spacing-left-large:1.92%;--awb-width-medium:100%;--awb-order-medium:0;--awb-margin-top-medium:0px;--awb-spacing-right-medium:1.92%;--awb-spacing-left-medium:1.92%;--awb-width-small:100%;--awb-order-small:0;--awb-margin-top-small:0px;--awb-spacing-right-small:1.92%;--awb-spacing-left-small:1.92%;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-center fusion-content-layout-row\"><div class=\"fusion-text fusion-text-1\"><h1 class=\"\" style=\"text-align: center; --fontsize: 48; line-height: 1.2;\" data-fontsize=\"48\" data-lineheight=\"57.6px\">Single Amino Acids<\/h1>\n<h2 class=\"\" style=\"text-align: center; --fontsize: 30; line-height: 1.2; --minfontsize: 30;\" data-fontsize=\"30\" data-lineheight=\"36px\"><\/h2>\n<\/div><\/div><\/div><\/div><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-2 fusion-flex-container has-pattern-background has-mask-background nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"--link_hover_color: var(--awb-custom_color_1);--awb-border-radius-top-left:0px;--awb-border-radius-top-right:0px;--awb-border-radius-bottom-right:0px;--awb-border-radius-bottom-left:0px;--awb-padding-right:40px;--awb-padding-bottom:0px;--awb-padding-left:40px;--awb-margin-top:30px;--awb-margin-bottom:30px;--awb-background-color:#ffffff;--awb-flex-wrap:wrap;\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-stretch fusion-flex-content-wrap\" style=\"max-width:1248px;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-1 fusion_builder_column_1_1 1_1 fusion-flex-column\" style=\"--awb-padding-top:30px;--awb-padding-right:40px;--awb-padding-left:40px;--awb-padding-right-small:20px;--awb-padding-left-small:20px;--awb-bg-color:var(--awb-color1);--awb-bg-color-hover:var(--awb-color1);--awb-bg-size:cover;--awb-width-large:100%;--awb-margin-top-large:30px;--awb-spacing-right-large:0.96%;--awb-margin-bottom-large:0px;--awb-spacing-left-large:0.96%;--awb-width-medium:100%;--awb-order-medium:0;--awb-spacing-right-medium:0.96%;--awb-spacing-left-medium:0.96%;--awb-width-small:100%;--awb-order-small:0;--awb-margin-top-small:0px;--awb-spacing-right-small:1.92%;--awb-spacing-left-small:1.92%;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-flex-start fusion-content-layout-column\"><div class=\"fusion-text fusion-text-2\"><div>\n<p>All single amino acids are foods for special medical purposes. They are suitable for use in the dietary management of disorders in amino acid metabolism or other diseases requiring supplementation with the corresponding amino acid. The single amino acid supplements are highly concentrated and are available either in tablet form and\/or in powder form. Especially the single amino acids in tablet form (minis) are odorless, tasteless and easy to swallow.   <\/p>\n<\/div>\n<div class=\"notranslate\" style=\"all: initial;\"><\/div>\n<\/div><\/div><\/div><\/div><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-3 fusion-flex-container nonhundred-percent-fullwidth non-hundred-percent-height-scrolling fusion-animated\" style=\"--link_hover_color: var(--awb-custom_color_1);--awb-border-radius-top-left:0px;--awb-border-radius-top-right:0px;--awb-border-radius-bottom-right:0px;--awb-border-radius-bottom-left:0px;--awb-padding-right:40px;--awb-padding-left:40px;--awb-margin-top:30px;--awb-margin-bottom:30px;--awb-background-color:#ffffff;--awb-flex-wrap:wrap;\" data-animationType=\"fadeInUp\" data-animationDuration=\"1.9\" data-animationOffset=\"top-into-view\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-stretch fusion-flex-content-wrap\" style=\"max-width:1248px;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-2 fusion_builder_column_1_1 1_1 fusion-flex-column fusion-flex-align-self-center\" style=\"--awb-bg-size:cover;--awb-width-large:100%;--awb-margin-top-large:0px;--awb-spacing-right-large:0%;--awb-margin-bottom-large:20px;--awb-spacing-left-large:0%;--awb-width-medium:100%;--awb-order-medium:0;--awb-spacing-right-medium:0%;--awb-spacing-left-medium:0%;--awb-width-small:100%;--awb-order-small:0;--awb-spacing-right-small:1.92%;--awb-spacing-left-small:1.92%;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-center fusion-content-layout-column\"><div class=\"fusion-separator fusion-full-width-sep\" style=\"align-self: center;margin-left: auto;margin-right: auto;margin-top:20px;width:100%;\"><\/div>\n<div class=\"table-1 difp-produktinformation difp-pdf-uebersetzung\">\n<p>&nbsp;<\/p>\n<p>&nbsp;<\/p>\n<table border=\"1\" width=\"100%\">\n<thead>\n<tr>\n<td>\n<h4 class=\"fusion-responsive-typography-calculated\" style=\"text-align: center; --fontsize: 18; line-height: 1.25; --minfontsize: 18;\" data-fontsize=\"18\" data-lineheight=\"22.5px\">Product<\/h4>\n<\/td>\n<td>\n<h4 class=\"fusion-responsive-typography-calculated\" style=\"text-align: center; --fontsize: 18; line-height: 1.25; --minfontsize: 18;\" data-fontsize=\"18\" data-lineheight=\"22.5px\">Dosage form<\/h4>\n<\/td>\n<td>\n<h4 class=\"fusion-responsive-typography-calculated\" style=\"text-align: center; --fontsize: 18; line-height: 1.25; --minfontsize: 18;\" data-fontsize=\"18\" data-lineheight=\"22.5px\">Amino acid specification<\/h4>\n<\/td>\n<td>\n<h4 class=\"fusion-responsive-typography-calculated\" style=\"text-align: center; --fontsize: 18; line-height: 1.25; --minfontsize: 18;\" data-fontsize=\"18\" data-lineheight=\"22.5px\">For dietary management of e.g.<\/h4>\n<\/td>\n<td>\n<h4 class=\"fusion-responsive-typography-calculated\" style=\"text-align: center; --fontsize: 18; line-height: 1.25; --minfontsize: 18;\" data-fontsize=\"18\" data-lineheight=\"22.5px\">Download PDF<\/h4>\n<\/td>\n<\/tr>\n<\/thead>\n<tbody>\n<tr>\n<td align=\"left\">Alanin<\/td>\n<td align=\"left\">Powder<\/td>\n<td align=\"left\">100 g L-alanine\/100 g<\/td>\n<td align=\"left\">Glycogenosis (GSD) type II\/Morbus Pompe<\/td>\n<td style=\"text-align: center;\"><a href=\"https:\/\/staging.metax.org\/wp-content\/uploads\/metax_de_pi_alanin.pdf\" target=\"_blank\" rel=\"noopener\">Download<\/a><\/td>\n<\/tr>\n<tr>\n<td><a href=\"https:\/\/staging.metax.org\/en\/urea-cycle-disorders-ucd\/arginine500-minis\/\">Arginin<sup>500<\/sup> minis<\/a><\/td>\n<td align=\"left\">Tablet form<\/td>\n<td align=\"left\">500 mg L-arginine\/tablet<\/td>\n<td align=\"left\">Urea Cycle Disorders<\/td>\n<td style=\"text-align: center;\" align=\"left\"><a href=\"https:\/\/staging.metax.org\/wp-content\/uploads\/metax_de_pi_arginin500_minis.pdf\" target=\"_blank\" rel=\"noopener\">Download<\/a><\/td>\n<\/tr>\n<tr>\n<td align=\"left\"><a href=\"https:\/\/staging.metax.org\/en\/urea-cycle-disorders-ucd\/citrullin500-minis\/\">Citrullin<sup>500<\/sup> minis<\/a><\/td>\n<td align=\"left\">Tablet form<\/td>\n<td align=\"left\">500 mg L-citrulline\/tablet<\/td>\n<td align=\"left\">Urea Cycle Disorders<\/td>\n<td style=\"text-align: center;\" align=\"left\"><a href=\"https:\/\/staging.metax.org\/wp-content\/uploads\/metax_de_pi_citrullin500_minis.pdf\" target=\"_blank\" rel=\"noopener\">Download<\/a><\/td>\n<\/tr>\n<tr>\n<td align=\"left\"><a href=\"https:\/\/staging.metax.org\/harnstoffzyklusstoerungen\/citrullin\/\">Citrullin<\/a><\/td>\n<td align=\"left\">Powder<\/td>\n<td align=\"left\">100 g L-citrulline\/100 g<\/td>\n<td align=\"left\">Urea Cycle Disorders<\/td>\n<td style=\"text-align: center;\" align=\"left\"><a href=\"https:\/\/staging.metax.org\/wp-content\/uploads\/metax_de_pi_citrullin.pdf\" target=\"_blank\" rel=\"noopener\">Download<\/a><\/td>\n<\/tr>\n<tr>\n<td align=\"left\"><a href=\"https:\/\/staging.metax.org\/en\/homocystinuria\/cystine\/\">Cystin<\/a><\/td>\n<td align=\"left\">Powder<\/td>\n<td align=\"left\">100 g L-cystine\/100 g<\/td>\n<td align=\"left\">Homocystinuria<\/td>\n<td style=\"text-align: center;\" align=\"left\"><a href=\"https:\/\/staging.metax.org\/wp-content\/uploads\/metax_de_pi_cystin.pdf\" target=\"_blank\" rel=\"noopener\">Download<\/a><\/td>\n<\/tr>\n<tr>\n<td align=\"left\"><a href=\"https:\/\/staging.metax.org\/en\/isovaleric-acidemia\/glycin500-minis\/\">Glycin<sup>500<\/sup> minis<\/a><\/td>\n<td align=\"left\">Tablet form<\/td>\n<td align=\"left\">500 mg L-glycine\/tablet<\/td>\n<td align=\"left\">Isovaleric acidemia (IVA), serine deficiency diseases, creatine transporter defect (CRTR-D)<\/td>\n<td style=\"text-align: center;\" align=\"left\"><a href=\"https:\/\/staging.metax.org\/wp-content\/uploads\/metax_de_pi_glycin500_minis.pdf\" target=\"_blank\" rel=\"noopener\">Download<\/a><\/td>\n<\/tr>\n<tr>\n<td align=\"left\"><a href=\"https:\/\/staging.metax.org\/en\/isovaleric-acidemia\/glycine\/\">Glycin<\/a><\/td>\n<td align=\"left\">Powder<\/td>\n<td align=\"left\">100 g L-glycine\/100 g<\/td>\n<td align=\"left\">Isovaleric acidemia (IVA), serine deficiency diseases, creatine transporter defect (CRTR-D)<\/td>\n<td style=\"text-align: center;\" align=\"left\"><a href=\"https:\/\/staging.metax.org\/wp-content\/uploads\/metax_de_pi_glycin.pdf\" target=\"_blank\" rel=\"noopener\">Download<\/a><\/td>\n<\/tr>\n<tr>\n<td align=\"left\"><a href=\"https:\/\/staging.metax.org\/en\/maple-syrup-disease-msud\/isoleucine100-minis\/\">Isoleucin<sup>100<\/sup> minis<\/a><\/td>\n<td align=\"left\">Tablet form<\/td>\n<td align=\"left\">100 mg L-isoleucine\/tablet<\/td>\n<td align=\"left\">MSUD, MMA, PA<\/td>\n<td style=\"text-align: center;\" align=\"left\"><a href=\"https:\/\/staging.metax.org\/wp-content\/uploads\/metax_de_pi_isoleucin100_minis.pdf\" target=\"_blank\" rel=\"noopener\">Download<\/a><\/td>\n<\/tr>\n<tr>\n<td align=\"left\"><a href=\"https:\/\/staging.metax.org\/en\/methylmalonic-aciduria-propionic-aciduria-mma-pa\/leucine\/\">Leucin<\/a><\/td>\n<td align=\"left\">Powder<\/td>\n<td align=\"left\">100 g L-leucine\/100 g<\/td>\n<td align=\"left\">MSUD, MMA, PA<\/td>\n<td style=\"text-align: center;\" align=\"left\"><a href=\"https:\/\/staging.metax.org\/wp-content\/uploads\/metax_de_pi_leucin.pdf\" target=\"_blank\" rel=\"noopener\">Download<\/a><\/td>\n<\/tr>\n<tr>\n<td align=\"left\">Lysine<sup>300<\/sup> minis<\/td>\n<td align=\"left\">Tablet form<\/td>\n<td align=\"left\">300 mg L-lysine\/tablet<\/td>\n<td align=\"left\">Hyperornithinemia-Hyperammonemia-Homocitrullinuria Syndrome (HHH), Lysinuric Protein Intolerance (LPI)<\/td>\n<td style=\"text-align: center;\" align=\"left\"><a href=\"https:\/\/staging.metax.org\/wp-content\/uploads\/metax_de_pi_lysin300_minis.pdf\" target=\"_blank\" rel=\"noopener\">Download<\/a><\/td>\n<\/tr>\n<tr>\n<td align=\"left\">Magnesium L-aspartate<\/td>\n<td align=\"left\">Powder<\/td>\n<td align=\"left\">69 g L-aspartic acid\/100 g<\/td>\n<td align=\"left\">mitochondrial aspartyl-trNA synthetase deficiency (DARS2 deficiency, LBSL)<\/td>\n<td style=\"text-align: center;\" align=\"left\"><a href=\"https:\/\/staging.metax.org\/wp-content\/uploads\/metax_de_pi_magnesium-l-aspartat.pdf\" target=\"_blank\" rel=\"noopener\">Download<\/a><\/td>\n<\/tr>\n<tr>\n<td align=\"left\">Methionine<\/td>\n<td align=\"left\">Powder<\/td>\n<td align=\"left\">100 g L-methionine\/100 g<\/td>\n<td align=\"left\">Methionyl-tRNA synthetase deficiency (MARS1 deficiency)<\/td>\n<td style=\"text-align: center;\" align=\"left\"><a href=\"https:\/\/staging.metax.org\/wp-content\/uploads\/metax_de_pi_methionin.pdf\" target=\"_blank\" rel=\"noopener\">Download<\/a><\/td>\n<\/tr>\n<tr>\n<td align=\"left\">Ornithin<\/td>\n<td align=\"left\">Powder<\/td>\n<td align=\"left\">78 g L-ornithine\/100 g<\/td>\n<td align=\"left\">Arginase-1 Deficiency, GAMT Deficiency<\/td>\n<td style=\"text-align: center;\" align=\"left\"><a href=\"https:\/\/staging.metax.org\/wp-content\/uploads\/metax_de_pi_ornithin.pdf\" target=\"_blank\" rel=\"noopener\">Download<\/a><\/td>\n<\/tr>\n<tr>\n<td align=\"left\"><a href=\"https:\/\/staging.metax.org\/en\/tyrosinemia\/phenylalanine50-minis\/\">Phenylalanin<sup>50<\/sup> minis<\/a><\/td>\n<td align=\"left\">Tablet form<\/td>\n<td align=\"left\">50 mg L-phenylalanine\/tablet<\/td>\n<td align=\"left\">Tyrosinemia, alkaptonuria, FARS2 defect<\/td>\n<td style=\"text-align: center;\" align=\"left\"><a href=\"https:\/\/staging.metax.org\/wp-content\/uploads\/metax_de_pi_phenylalanin50_minis.pdf\" target=\"_blank\" rel=\"noopener\">Download<\/a><\/td>\n<\/tr>\n<tr>\n<td align=\"left\"><a href=\"https:\/\/staging.metax.org\/en\/tyrosinemia\/phenylalanine\/\">Phenylalanin<\/a><\/td>\n<td align=\"left\">Powder<\/td>\n<td align=\"left\">100 g L-phenylalanine\/100 g<\/td>\n<td align=\"left\">Tyrosinemia, alkaptonuria, FARS2 defect<\/td>\n<td style=\"text-align: center;\" align=\"left\"><a href=\"https:\/\/staging.metax.org\/wp-content\/uploads\/metax_de_pi_phenylalanin.pdf\" target=\"_blank\" rel=\"noopener\">Download<\/a><\/td>\n<\/tr>\n<tr>\n<td align=\"left\">Serin<sup>500<\/sup> minis<\/td>\n<td align=\"left\">Tablet form<\/td>\n<td align=\"left\">500 mg L-serine\/tablet<\/td>\n<td align=\"left\">GRIN2B-associated encephalopathy or serine deficiency diseases<\/td>\n<td style=\"text-align: center;\" align=\"left\"><a href=\"https:\/\/staging.metax.org\/wp-content\/uploads\/metax_de_pi_serin500_minis.pdf\" target=\"_blank\" rel=\"noopener\">Download<\/a><\/td>\n<\/tr>\n<tr>\n<td align=\"left\">Serin<\/td>\n<td align=\"left\">Powder<\/td>\n<td align=\"left\">100 g L-serine\/100 g<\/td>\n<td align=\"left\">GRIN2B-associated encephalopathy or serine deficiency diseases<\/td>\n<td style=\"text-align: center;\" align=\"left\"><a href=\"https:\/\/staging.metax.org\/wp-content\/uploads\/metax_de_pi_serin.pdf\" target=\"_blank\" rel=\"noopener\">Download<\/a><\/td>\n<\/tr>\n<tr>\n<td align=\"left\">Tryptophan<\/td>\n<td align=\"left\">Powder<\/td>\n<td align=\"left\">100 g L-tryptophan\/100 g<\/td>\n<td align=\"left\">Pyridoxine-Dependent Epilepsy (PDE)<\/td>\n<td style=\"text-align: center;\" align=\"left\"><a href=\"https:\/\/staging.metax.org\/wp-content\/uploads\/metax_de_pi_tryptophan.pdf\" target=\"_blank\" rel=\"noopener\">Download<\/a><\/td>\n<\/tr>\n<tr>\n<td align=\"left\"><a href=\"https:\/\/staging.metax.org\/en\/phenylketonuria\/tyrosine\/\">Tyrosin<\/a><\/td>\n<td align=\"left\">Powder<\/td>\n<td align=\"left\">100 g L-tyrosine\/100 g<\/td>\n<td align=\"left\">PKU, HPA<\/td>\n<td style=\"text-align: center;\" align=\"left\"><a href=\"https:\/\/staging.metax.org\/wp-content\/uploads\/metax_de_pi_tyrosin.pdf\" target=\"_blank\" rel=\"noopener\">Download<\/a><\/td>\n<\/tr>\n<tr>\n<td align=\"left\"><a href=\"https:\/\/staging.metax.org\/en\/maple-syrup-disease-msud\/valin100-minis\/\">Valin<sup>100<\/sup> minis<\/a><\/td>\n<td align=\"left\">Tablet form<\/td>\n<td align=\"left\">100 mg L-valine\/tablet<\/td>\n<td align=\"left\">MSUD, MMA, PA<\/td>\n<td style=\"text-align: center;\" align=\"left\"><a href=\"https:\/\/staging.metax.org\/wp-content\/uploads\/metax_de_pi_valin100_minis.pdf\" target=\"_blank\" rel=\"noopener\">Download<\/a><\/td>\n<\/tr>\n<tr>\n<td align=\"left\"><a href=\"https:\/\/staging.metax.org\/en\/maple-syrup-disease-msud\/valine\/\">Valin<\/a><\/td>\n<td align=\"left\">Powder<\/td>\n<td align=\"left\">100 mg L-Valin\/100 g<\/td>\n<td align=\"left\">MSUD, MMA, PA<\/td>\n<td style=\"text-align: center;\" align=\"left\"><a href=\"https:\/\/staging.metax.org\/wp-content\/uploads\/metax_de_pi_valin.pdf\" target=\"_blank\" rel=\"noopener\">Download<\/a><\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n<\/div>\n<div class=\"fusion-separator fusion-full-width-sep\" style=\"align-self: center;margin-left: auto;margin-right: auto;margin-top:20px;width:100%;\"><div class=\"fusion-separator-border sep-single sep-solid\" style=\"--awb-height:20px;--awb-amount:20px;--awb-sep-color:var(--awb-color2);border-color:var(--awb-color2);border-top-width:1px;\"><\/div><\/div><\/div><\/div><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-3 fusion_builder_column_1_1 1_1 fusion-flex-column\" style=\"--awb-bg-size:cover;--awb-width-large:100%;--awb-margin-top-large:60px;--awb-spacing-right-large:1.92%;--awb-margin-bottom-large:0px;--awb-spacing-left-large:1.92%;--awb-width-medium:100%;--awb-order-medium:0;--awb-spacing-right-medium:1.92%;--awb-spacing-left-medium:1.92%;--awb-width-small:100%;--awb-order-small:0;--awb-spacing-right-small:1.92%;--awb-spacing-left-small:1.92%;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-flex-start fusion-content-layout-column\"><div class=\"fusion-title title fusion-title-1 fusion-sep-none fusion-title-center fusion-title-text fusion-title-size-three\" style=\"--awb-margin-top-small:10px;--awb-margin-right-small:0px;--awb-margin-bottom-small:10px;--awb-margin-left-small:0px;\"><h3 class=\"fusion-title-heading title-heading-center fusion-responsive-typography-calculated\" style=\"margin:0;--fontSize:24;--minFontSize:24;line-height:var(--awb-typography1-line-height);\">Discover our single amino acids in tablet form<\/h3><\/div><div class=\"fusion-image-carousel fusion-image-carousel-auto fusion-image-carousel-1 awb-image-carousel-top-below-caption\"><div class=\"awb-carousel awb-swiper awb-swiper-carousel awb-carousel--carousel awb-swiper-dots-position-bottom awb-imageframe-style awb-imageframe-style-below awb-imageframe-style-1\" data-layout=\"carousel\" data-autoplay=\"yes\" data-autoplayspeed=\"2500\" data-autoplaypause=\"no\" data-columns=\"4\" data-columnsmedium=\"1\" data-columnssmall=\"1\" data-itemmargin=\"13\" data-itemwidth=\"180\" data-touchscroll=\"no\" data-freemode=\"no\" data-imagesize=\"auto\" data-scrollitems=\"1\" data-centeredslides=\"no\" data-rotationangle=\"50\" data-depth=\"100\" data-speed=\"500\" data-shadow=\"no\" data-pagination=\"bullets\" style=\"--awb-columns:4;\"><div class=\"swiper-wrapper awb-image-carousel-wrapper fusion-flex-align-items-center\"><div class=\"swiper-slide\"><div class=\"fusion-carousel-item-wrapper\"><div class=\"fusion-image-wrapper hover-type-none\"><a href=\"https:\/\/staging.metax.org\/en\/maple-syrup-disease-msud\/isoleucine100-minis\/\" target=\"_self\"><img loading=\"lazy\" decoding=\"async\" width=\"540\" height=\"340\" src=\"https:\/\/staging.metax.org\/wp-content\/uploads\/isoleucin_100_minis_mit_verlauf.jpg\" class=\"attachment-full size-full\" alt=\"Isoleucin100 minis\" srcset=\"https:\/\/staging.metax.org\/wp-content\/uploads\/isoleucin_100_minis_mit_verlauf-200x126.jpg 200w, https:\/\/staging.metax.org\/wp-content\/uploads\/isoleucin_100_minis_mit_verlauf-400x252.jpg 400w, https:\/\/staging.metax.org\/wp-content\/uploads\/isoleucin_100_minis_mit_verlauf.jpg 540w\" sizes=\"auto, (min-width: 2200px) 100vw, (min-width: 736px) 290px, (min-width: 704px) 387px, (min-width: 672px) 581px, (min-width: 640px) 672px, \" \/><\/a><\/div><div class=\"awb-imageframe-caption-container\"><div class=\"awb-imageframe-caption\"><h3 class=\"awb-imageframe-caption-title\">Isoleucin100 minis<\/h3><p class=\"awb-imageframe-caption-text\">single amino acid<\/p><\/div><\/div><\/div><\/div><div class=\"swiper-slide\"><div class=\"fusion-carousel-item-wrapper\"><div class=\"fusion-image-wrapper hover-type-none\"><a href=\"https:\/\/staging.metax.org\/en\/tyrosinemia\/phenylalanine50-minis\/\" target=\"_self\"><img loading=\"lazy\" decoding=\"async\" width=\"540\" height=\"340\" src=\"https:\/\/staging.metax.org\/wp-content\/uploads\/phenylalanin_50_minis_mit_verlauf.jpg\" class=\"attachment-full size-full\" alt=\"Phenylalanine50 minis\" srcset=\"https:\/\/staging.metax.org\/wp-content\/uploads\/phenylalanin_50_minis_mit_verlauf-200x126.jpg 200w, https:\/\/staging.metax.org\/wp-content\/uploads\/phenylalanin_50_minis_mit_verlauf-400x252.jpg 400w, https:\/\/staging.metax.org\/wp-content\/uploads\/phenylalanin_50_minis_mit_verlauf.jpg 540w\" sizes=\"auto, (min-width: 2200px) 100vw, (min-width: 736px) 290px, (min-width: 704px) 387px, (min-width: 672px) 581px, (min-width: 640px) 672px, \" \/><\/a><\/div><div class=\"awb-imageframe-caption-container\"><div class=\"awb-imageframe-caption\"><h3 class=\"awb-imageframe-caption-title\">Phenylalanine50 minis<\/h3><p class=\"awb-imageframe-caption-text\">single amino acid<\/p><\/div><\/div><\/div><\/div><div class=\"swiper-slide\"><div class=\"fusion-carousel-item-wrapper\"><div class=\"fusion-image-wrapper hover-type-none\"><a href=\"https:\/\/staging.metax.org\/en\/urea-cycle-disorders-ucd\/arginine500-minis\/\" target=\"_self\"><img loading=\"lazy\" decoding=\"async\" width=\"540\" height=\"340\" src=\"https:\/\/staging.metax.org\/wp-content\/uploads\/arginin500_mit_verlauf.jpg\" class=\"attachment-full size-full\" alt=\"Arginin500 minis\" srcset=\"https:\/\/staging.metax.org\/wp-content\/uploads\/arginin500_mit_verlauf-200x126.jpg 200w, https:\/\/staging.metax.org\/wp-content\/uploads\/arginin500_mit_verlauf-400x252.jpg 400w, https:\/\/staging.metax.org\/wp-content\/uploads\/arginin500_mit_verlauf.jpg 540w\" sizes=\"auto, (min-width: 2200px) 100vw, (min-width: 736px) 290px, (min-width: 704px) 387px, (min-width: 672px) 581px, (min-width: 640px) 672px, \" \/><\/a><\/div><div class=\"awb-imageframe-caption-container\"><div class=\"awb-imageframe-caption\"><h3 class=\"awb-imageframe-caption-title\">Arginin500 minis<\/h3><p class=\"awb-imageframe-caption-text\">single amino acid<\/p><\/div><\/div><\/div><\/div><div class=\"swiper-slide\"><div class=\"fusion-carousel-item-wrapper\"><div class=\"fusion-image-wrapper hover-type-none\"><a href=\"https:\/\/staging.metax.org\/en\/urea-cycle-disorders-ucd\/citrullin500-minis\/\" target=\"_self\"><img loading=\"lazy\" decoding=\"async\" width=\"540\" height=\"340\" src=\"https:\/\/staging.metax.org\/wp-content\/uploads\/citrullin_mit_verlauf.jpg\" class=\"attachment-full size-full\" alt=\"Citrullin500 minis\" srcset=\"https:\/\/staging.metax.org\/wp-content\/uploads\/citrullin_mit_verlauf-200x126.jpg 200w, https:\/\/staging.metax.org\/wp-content\/uploads\/citrullin_mit_verlauf-400x252.jpg 400w, https:\/\/staging.metax.org\/wp-content\/uploads\/citrullin_mit_verlauf.jpg 540w\" sizes=\"auto, (min-width: 2200px) 100vw, (min-width: 736px) 290px, (min-width: 704px) 387px, (min-width: 672px) 581px, (min-width: 640px) 672px, \" \/><\/a><\/div><div class=\"awb-imageframe-caption-container\"><div class=\"awb-imageframe-caption\"><h3 class=\"awb-imageframe-caption-title\">Citrullin500 minis<\/h3><p class=\"awb-imageframe-caption-text\">single amino acid<\/p><\/div><\/div><\/div><\/div><div class=\"swiper-slide\"><div class=\"fusion-carousel-item-wrapper\"><div class=\"fusion-image-wrapper hover-type-none\"><a href=\"https:\/\/staging.metax.org\/en\/maple-syrup-disease-msud\/valin100-minis\/\" target=\"_self\"><img loading=\"lazy\" decoding=\"async\" width=\"540\" height=\"340\" src=\"https:\/\/staging.metax.org\/wp-content\/uploads\/valin_100_minis_mit_verlauf.jpg\" class=\"attachment-full size-full\" alt=\"Valin100 minis\" srcset=\"https:\/\/staging.metax.org\/wp-content\/uploads\/valin_100_minis_mit_verlauf-200x126.jpg 200w, https:\/\/staging.metax.org\/wp-content\/uploads\/valin_100_minis_mit_verlauf-400x252.jpg 400w, https:\/\/staging.metax.org\/wp-content\/uploads\/valin_100_minis_mit_verlauf.jpg 540w\" sizes=\"auto, (min-width: 2200px) 100vw, (min-width: 736px) 290px, (min-width: 704px) 387px, (min-width: 672px) 581px, (min-width: 640px) 672px, \" \/><\/a><\/div><div class=\"awb-imageframe-caption-container\"><div class=\"awb-imageframe-caption\"><h3 class=\"awb-imageframe-caption-title\">Valin100 minis<\/h3><p class=\"awb-imageframe-caption-text\">single amino acid<\/p><\/div><\/div><\/div><\/div><\/div><div class=\"awb-swiper-button awb-swiper-button-prev\"><i class=\"awb-icon-angle-left\" aria-hidden=\"true\"><\/i><\/div><div class=\"awb-swiper-button awb-swiper-button-next\"><i class=\"awb-icon-angle-right\" aria-hidden=\"true\"><\/i><\/div><\/div><\/div><\/div><\/div><\/div><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-4 fusion-flex-container nonhundred-percent-fullwidth non-hundred-percent-height-scrolling fusion-animated\" style=\"--link_hover_color: var(--awb-custom_color_1);--awb-border-radius-top-left:0px;--awb-border-radius-top-right:0px;--awb-border-radius-bottom-right:0px;--awb-border-radius-bottom-left:0px;--awb-margin-top:30px;--awb-margin-bottom:30px;--awb-flex-wrap:wrap;\" data-animationType=\"fadeInUp\" data-animationDuration=\"1.9\" data-animationOffset=\"top-into-view\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-stretch fusion-flex-content-wrap\" style=\"max-width:1248px;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-4 fusion_builder_column_1_3 1_3 fusion-flex-column\" style=\"--awb-padding-top:10px;--awb-padding-bottom:10px;--awb-bg-color:var(--awb-color1);--awb-bg-color-hover:var(--awb-color1);--awb-bg-size:cover;--awb-width-large:33.333333333333%;--awb-margin-top-large:0px;--awb-spacing-right-large:0%;--awb-margin-bottom-large:20px;--awb-spacing-left-large:2.88%;--awb-width-medium:33.333333333333%;--awb-order-medium:0;--awb-spacing-right-medium:0%;--awb-spacing-left-medium:2.88%;--awb-width-small:100%;--awb-order-small:0;--awb-spacing-right-small:1.92%;--awb-spacing-left-small:1.92%;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-space-between fusion-content-layout-column\"><div class=\"fusion-image-element \" style=\"text-align:center;--awb-caption-title-font-family:var(--h2_typography-font-family);--awb-caption-title-font-weight:var(--h2_typography-font-weight);--awb-caption-title-font-style:var(--h2_typography-font-style);--awb-caption-title-size:var(--h2_typography-font-size);--awb-caption-title-transform:var(--h2_typography-text-transform);--awb-caption-title-line-height:var(--h2_typography-line-height);--awb-caption-title-letter-spacing:var(--h2_typography-letter-spacing);\"><span class=\" fusion-imageframe imageframe-none imageframe-1 hover-type-none difp-pdf-uebersetzung\"><a class=\"fusion-no-lightbox\" href=\"https:\/\/staging.metax.org\/wp-content\/uploads\/metax_de_ues_einzelas.pdf\" target=\"_blank\" aria-label=\"Product overview &#8211; single amino acid supplements for &#8220;rare metabolic disorders&#8221;\" rel=\"noopener noreferrer\"><img loading=\"lazy\" decoding=\"async\" width=\"300\" height=\"215\" alt=\"Overview of single amino acid supplements\" src=\"https:\/\/staging.metax.org\/wp-content\/uploads\/einzel_as_produktuebersicht_thumb_de.jpg\" class=\"img-responsive wp-image-18441\" srcset=\"https:\/\/staging.metax.org\/wp-content\/uploads\/einzel_as_produktuebersicht_thumb_de-200x143.jpg 200w, https:\/\/staging.metax.org\/wp-content\/uploads\/einzel_as_produktuebersicht_thumb_de.jpg 300w\" sizes=\"auto, (max-width: 640px) 100vw, 300px\" \/><\/a><\/span><\/div><\/div><\/div><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-5 fusion_builder_column_2_3 2_3 fusion-flex-column fusion-column-inner-bg-wrapper difp-pdf-uebersetzung\" style=\"--awb-padding-top:20px;--awb-padding-right:20px;--awb-padding-left:20px;--awb-inner-bg-color:var(--awb-color1);--awb-inner-bg-color-hover:var(--awb-color1);--awb-inner-bg-size:cover;--awb-width-large:66.666666666667%;--awb-margin-top-large:0px;--awb-spacing-right-large:1.44%;--awb-margin-bottom-large:20px;--awb-spacing-left-large:0px;--awb-width-medium:66.666666666667%;--awb-order-medium:0;--awb-spacing-right-medium:1.44%;--awb-spacing-left-medium:0px;--awb-width-small:100%;--awb-order-small:0;--awb-spacing-right-small:1.92%;--awb-spacing-left-small:1.92%;\"><span class=\"fusion-column-inner-bg hover-type-none\"><a class=\"fusion-column-anchor\" href=\"https:\/\/staging.metax.org\/wp-content\/uploads\/metax_de_ues_einzelas.pdf\" rel=\"noopener noreferrer\" target=\"_blank\"><span class=\"fusion-column-inner-bg-image\"><\/span><\/a><\/span><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-space-between fusion-content-layout-column\"><div class=\"fusion-text fusion-text-3\"><h2 class=\"fusion-responsive-typography-calculated\" style=\"text-align: center; --fontsize: 26; line-height: 1.2; --minfontsize: 26;\" data-fontsize=\"26\" data-lineheight=\"31.2px\">Overview of single amino acid supplements for &#8220;rare metabolic disorders&#8221;<\/h2>\n<p>Single amino acids &#8211; in powder and tablet form (minis), if supplementation with the single amino acid in question is indicated.<\/p>\n<\/div><div style=\"text-align:center;\"><a class=\"fusion-button button-flat fusion-button-default-size button-default fusion-button-default button-1 fusion-button-default-span fusion-button-default-type\" style=\"--button_margin-bottom:10px;\" target=\"_blank\" rel=\"noopener noreferrer\"><span class=\"fusion-button-text awb-button__text awb-button__text--default\">Download overview of single amino acid supplements (PDF)<\/span><\/a><\/div><\/div><\/div><\/div><\/div><\/p>\n","protected":false},"excerpt":{"rendered":"","protected":false},"author":19,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"footnotes":""},"class_list":["post-18439","page","type-page","status-publish","hentry"],"_links":{"self":[{"href":"https:\/\/staging.metax.org\/en\/wp-json\/wp\/v2\/pages\/18439","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/staging.metax.org\/en\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/staging.metax.org\/en\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/staging.metax.org\/en\/wp-json\/wp\/v2\/users\/19"}],"replies":[{"embeddable":true,"href":"https:\/\/staging.metax.org\/en\/wp-json\/wp\/v2\/comments?post=18439"}],"version-history":[{"count":8,"href":"https:\/\/staging.metax.org\/en\/wp-json\/wp\/v2\/pages\/18439\/revisions"}],"predecessor-version":[{"id":21594,"href":"https:\/\/staging.metax.org\/en\/wp-json\/wp\/v2\/pages\/18439\/revisions\/21594"}],"wp:attachment":[{"href":"https:\/\/staging.metax.org\/en\/wp-json\/wp\/v2\/media?parent=18439"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}