{"id":18418,"date":"2022-05-16T17:24:17","date_gmt":"2022-05-16T15:24:17","guid":{"rendered":"https:\/\/staging.metax.org\/glutaric-aciduria-type-i\/"},"modified":"2026-01-04T22:08:26","modified_gmt":"2026-01-04T21:08:26","slug":"glutaric-aciduria-type-i","status":"publish","type":"page","link":"https:\/\/staging.metax.org\/en\/glutaric-aciduria-type-i\/","title":{"rendered":"Glutaric Aciduria Type I"},"content":{"rendered":"<p><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-1 fusion-flex-container nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"--awb-border-sizes-top:0px;--awb-border-sizes-bottom:0px;--awb-border-sizes-left:0px;--awb-border-sizes-right:0px;--awb-border-color:var(--awb-custom_color_2);--awb-border-radius-top-left:0px;--awb-border-radius-top-right:0px;--awb-border-radius-bottom-right:0px;--awb-border-radius-bottom-left:0px;--awb-padding-top:0px;--awb-padding-right:0px;--awb-padding-bottom:0px;--awb-padding-left:0px;--awb-padding-top-medium:0px;--awb-margin-top:48px;--awb-margin-bottom:0px;--awb-margin-top-medium:0px;--awb-flex-wrap:wrap;\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-flex-start fusion-flex-align-content-flex-start fusion-flex-content-wrap\" style=\"max-width:1248px;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-0 fusion_builder_column_1_1 1_1 fusion-flex-column fusion-flex-align-self-flex-start\" style=\"--awb-padding-top:14px;--awb-padding-right-small:0px;--awb-bg-image:radial-gradient(circle at center center, var(--awb-color1) 0%,var(--awb-color4) 100%);--awb-bg-size:cover;--awb-width-large:100%;--awb-margin-top-large:0px;--awb-spacing-right-large:0.96%;--awb-margin-bottom-large:0px;--awb-spacing-left-large:0.96%;--awb-width-medium:100%;--awb-order-medium:0;--awb-margin-top-medium:0px;--awb-spacing-right-medium:0.96%;--awb-spacing-left-medium:0.96%;--awb-width-small:100%;--awb-order-small:0;--awb-margin-top-small:0px;--awb-spacing-right-small:1.92%;--awb-spacing-left-small:1.92%;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-center fusion-content-layout-row\"><div class=\"fusion-text fusion-text-1\"><h1 class=\"\" style=\"text-align: center;\" data-fontsize=\"48\" data-lineheight=\"57.6px\">ZeroLys<\/h1>\n<h2 class=\"\" style=\"text-align: center;\" data-fontsize=\"30\" data-lineheight=\"36px\">for Glutaric Aciduria Type I<\/h2>\n<\/div><\/div><\/div><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-1 fusion_builder_column_1_1 1_1 fusion-flex-column\" style=\"--awb-padding-top:30px;--awb-padding-right:40px;--awb-padding-bottom:20px;--awb-padding-left:40px;--awb-padding-right-small:20px;--awb-padding-left-small:20px;--awb-bg-color:var(--awb-color1);--awb-bg-color-hover:var(--awb-color1);--awb-bg-size:cover;--awb-width-large:100%;--awb-margin-top-large:30px;--awb-spacing-right-large:0.96%;--awb-margin-bottom-large:0px;--awb-spacing-left-large:0.96%;--awb-width-medium:100%;--awb-order-medium:0;--awb-spacing-right-medium:0.96%;--awb-spacing-left-medium:0.96%;--awb-width-small:100%;--awb-order-small:0;--awb-margin-top-small:0px;--awb-spacing-right-small:1.92%;--awb-spacing-left-small:1.92%;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-flex-start fusion-content-layout-column\"><div class=\"fusion-text fusion-text-2\"><p>All ZeroLys products are concentrated, mostly highly concentrated lysine (Lys)-free, tryptophan-reduced and arginine-enriched mixtures of highly purified L-amino acids. ZeroLys products are balanced diets for use in the dietary management of Glutaric Aciduria Type I \u2013 enriched with vitamins, minerals and trace elements.<\/p>\n<\/div><\/div><\/div><\/div><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-2 fusion-flex-container has-pattern-background has-mask-background nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"--link_hover_color: var(--awb-custom_color_1);--awb-border-radius-top-left:0px;--awb-border-radius-top-right:0px;--awb-border-radius-bottom-right:0px;--awb-border-radius-bottom-left:0px;--awb-margin-top:30px;--awb-margin-bottom:30px;--awb-flex-wrap:wrap;\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-stretch fusion-flex-content-wrap\" style=\"max-width:1248px;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-2 fusion_builder_column_1_3 1_3 fusion-flex-column fusion-column-inner-bg-wrapper schrift\" style=\"--awb-inner-bg-color:var(--awb-color1);--awb-inner-bg-color-hover:var(--awb-color1);--awb-inner-bg-size:cover;--awb-width-large:33.333333333333%;--awb-margin-top-large:1%;--awb-spacing-right-large:2.88%;--awb-margin-bottom-large:1%;--awb-spacing-left-large:2.88%;--awb-width-medium:33.333333333333%;--awb-order-medium:0;--awb-spacing-right-medium:2.88%;--awb-spacing-left-medium:2.88%;--awb-width-small:100%;--awb-order-small:0;--awb-spacing-right-small:1.92%;--awb-spacing-left-small:1.92%;\"><span class=\"fusion-column-inner-bg hover-type-none\"><a class=\"fusion-column-anchor\" href=\"https:\/\/staging.metax.org\/en\/glutaric-aciduria-type-i\/zerolys-infant-mixlcp\/\"><span class=\"fusion-column-inner-bg-image\"><\/span><\/a><\/span><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-center fusion-content-layout-row fusion-flex-align-items-stretch\"><div class=\"fusion-image-element \" style=\"text-align:center;--awb-caption-title-font-family:var(--h2_typography-font-family);--awb-caption-title-font-weight:var(--h2_typography-font-weight);--awb-caption-title-font-style:var(--h2_typography-font-style);--awb-caption-title-size:var(--h2_typography-font-size);--awb-caption-title-transform:var(--h2_typography-text-transform);--awb-caption-title-line-height:var(--h2_typography-line-height);--awb-caption-title-letter-spacing:var(--h2_typography-letter-spacing);\"><span class=\" fusion-imageframe imageframe-none imageframe-1 hover-type-none\"><img loading=\"lazy\" decoding=\"async\" width=\"540\" height=\"340\" alt=\"ZeroLys Infant Mix\" title=\"ZeroLys Infant MixLCP can\" src=\"https:\/\/staging.metax.org\/wp-content\/uploads\/zero_lys_infant_mit_verlauf.jpg\" class=\"img-responsive wp-image-18421\" srcset=\"https:\/\/staging.metax.org\/wp-content\/uploads\/zero_lys_infant_mit_verlauf-200x126.jpg 200w, https:\/\/staging.metax.org\/wp-content\/uploads\/zero_lys_infant_mit_verlauf-400x252.jpg 400w, https:\/\/staging.metax.org\/wp-content\/uploads\/zero_lys_infant_mit_verlauf.jpg 540w\" sizes=\"auto, (max-width: 640px) 100vw, 400px\" \/><\/span><\/div><div class=\"fusion-text fusion-text-3\" style=\"--awb-margin-top:20px;\"><h2 class=\"fusion-responsive-typography-calculated\" style=\"text-align: center; --fontsize: 26; line-height: 1.2; --minfontsize: 26;\" data-fontsize=\"26\" data-lineheight=\"31.2px\">ZeroLys Infant Mix<sup>LCP<\/sup><\/h2>\n<p style=\"text-align: center;\">infant formula<br \/>from birth onwards<\/p>\n<\/div><div class=\"fusion-text fusion-text-4\"><\/div><\/div><\/div><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-3 fusion_builder_column_1_3 1_3 fusion-flex-column fusion-column-inner-bg-wrapper schrift\" style=\"--awb-inner-bg-color:var(--awb-color1);--awb-inner-bg-color-hover:var(--awb-color1);--awb-inner-bg-size:cover;--awb-width-large:33.333333333333%;--awb-margin-top-large:1%;--awb-spacing-right-large:2.88%;--awb-margin-bottom-large:1%;--awb-spacing-left-large:2.88%;--awb-width-medium:33.333333333333%;--awb-order-medium:0;--awb-spacing-right-medium:2.88%;--awb-spacing-left-medium:2.88%;--awb-width-small:100%;--awb-order-small:0;--awb-spacing-right-small:1.92%;--awb-spacing-left-small:1.92%;\"><span class=\"fusion-column-inner-bg hover-type-none\"><a class=\"fusion-column-anchor\" href=\"https:\/\/staging.metax.org\/en\/glutaric-aciduria-type-i\/zerolys-minis\/\"><span class=\"fusion-column-inner-bg-image\"><\/span><\/a><\/span><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-center fusion-content-layout-row fusion-flex-align-items-stretch\"><div class=\"fusion-image-element \" style=\"text-align:center;--awb-caption-title-font-family:var(--h2_typography-font-family);--awb-caption-title-font-weight:var(--h2_typography-font-weight);--awb-caption-title-font-style:var(--h2_typography-font-style);--awb-caption-title-size:var(--h2_typography-font-size);--awb-caption-title-transform:var(--h2_typography-text-transform);--awb-caption-title-line-height:var(--h2_typography-line-height);--awb-caption-title-letter-spacing:var(--h2_typography-letter-spacing);\"><span class=\" fusion-imageframe imageframe-none imageframe-2 hover-type-none\"><img loading=\"lazy\" decoding=\"async\" width=\"540\" height=\"340\" alt=\"ZeroLys minis\" title=\"ZeroLys minis folding box\" src=\"https:\/\/staging.metax.org\/wp-content\/uploads\/zero_lys_minis_mit_verlauf.jpg\" class=\"img-responsive wp-image-18422\" srcset=\"https:\/\/staging.metax.org\/wp-content\/uploads\/zero_lys_minis_mit_verlauf-200x126.jpg 200w, https:\/\/staging.metax.org\/wp-content\/uploads\/zero_lys_minis_mit_verlauf-400x252.jpg 400w, https:\/\/staging.metax.org\/wp-content\/uploads\/zero_lys_minis_mit_verlauf.jpg 540w\" sizes=\"auto, (max-width: 640px) 100vw, 400px\" \/><\/span><\/div><div class=\"fusion-text fusion-text-5\" style=\"--awb-margin-top:20px;\"><h2 class=\"fusion-responsive-typography-calculated\" style=\"text-align: center; --fontsize: 26; line-height: 1.2; --minfontsize: 26;\" data-fontsize=\"26\" data-lineheight=\"31.2px\">ZeroLys minis<\/h2>\n<p style=\"text-align: center;\">in tablet form<br \/>from 3 years<\/p>\n<\/div><div class=\"fusion-text fusion-text-6\"><\/div><\/div><\/div><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-4 fusion_builder_column_1_3 1_3 fusion-flex-column fusion-column-inner-bg-wrapper difp-pdf-uebersetzung\" style=\"--awb-padding-top:20px;--awb-padding-right:20px;--awb-padding-left:20px;--awb-inner-bg-color:var(--awb-color1);--awb-inner-bg-color-hover:var(--awb-color1);--awb-inner-bg-size:cover;--awb-width-large:33.333333333333%;--awb-margin-top-large:1%;--awb-spacing-right-large:2.88%;--awb-margin-bottom-large:1%;--awb-spacing-left-large:2.88%;--awb-width-medium:33.333333333333%;--awb-order-medium:0;--awb-spacing-right-medium:2.88%;--awb-spacing-left-medium:2.88%;--awb-width-small:100%;--awb-order-small:0;--awb-spacing-right-small:1.92%;--awb-spacing-left-small:1.92%;\"><span class=\"fusion-column-inner-bg hover-type-none\"><a class=\"fusion-column-anchor\" href=\"https:\/\/staging.metax.org\/wp-content\/uploads\/metax_de_pi_zero_systeme.pdf\" rel=\"noopener noreferrer\" target=\"_blank\"><span class=\"fusion-column-inner-bg-image\"><\/span><\/a><\/span><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-space-between fusion-content-layout-column\"><div class=\"fusion-image-element \" style=\"text-align:center;--awb-caption-title-font-family:var(--h2_typography-font-family);--awb-caption-title-font-weight:var(--h2_typography-font-weight);--awb-caption-title-font-style:var(--h2_typography-font-style);--awb-caption-title-size:var(--h2_typography-font-size);--awb-caption-title-transform:var(--h2_typography-text-transform);--awb-caption-title-line-height:var(--h2_typography-line-height);--awb-caption-title-letter-spacing:var(--h2_typography-letter-spacing);\"><span class=\" fusion-imageframe imageframe-none imageframe-3 hover-type-none\"><img loading=\"lazy\" decoding=\"async\" width=\"300\" height=\"215\" alt=\"Product overview - Zero systems\" title=\"zero product overview thumbnail\" src=\"https:\/\/staging.metax.org\/wp-content\/uploads\/de_zero_produktuebersicht_thumb-1.jpg\" class=\"img-responsive wp-image-20145\" srcset=\"https:\/\/staging.metax.org\/wp-content\/uploads\/de_zero_produktuebersicht_thumb-1-200x143.jpg 200w, https:\/\/staging.metax.org\/wp-content\/uploads\/de_zero_produktuebersicht_thumb-1.jpg 300w\" sizes=\"auto, (max-width: 640px) 100vw, 300px\" \/><\/span><\/div><div class=\"fusion-text fusion-text-7\" style=\"--awb-margin-top:20px;\"><h2 class=\"\" style=\"text-align: center; --fontsize: 26; line-height: 1.2; --minfontsize: 26;\" data-fontsize=\"26\" data-lineheight=\"31.2px\">Overview of Zero systems<\/h2>\n<p style=\"text-align: center;\">Amino acid mixtures for the &#8220;rare&#8221; inborn errors of protein metabolism.<\/p>\n<\/div><div style=\"text-align:center;\"><a class=\"fusion-button button-flat fusion-button-default-size button-default fusion-button-default button-1 fusion-button-default-span fusion-button-default-type\" style=\"--button_margin-bottom:10px;\" target=\"_blank\" rel=\"noopener noreferrer\"><span class=\"fusion-button-text awb-button__text awb-button__text--default\">Download product overview (PDF)<\/span><\/a><\/div><\/div><\/div><\/div><\/div><\/p>\n","protected":false},"excerpt":{"rendered":"","protected":false},"author":19,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"footnotes":""},"class_list":["post-18418","page","type-page","status-publish","hentry"],"_links":{"self":[{"href":"https:\/\/staging.metax.org\/en\/wp-json\/wp\/v2\/pages\/18418","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/staging.metax.org\/en\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/staging.metax.org\/en\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/staging.metax.org\/en\/wp-json\/wp\/v2\/users\/19"}],"replies":[{"embeddable":true,"href":"https:\/\/staging.metax.org\/en\/wp-json\/wp\/v2\/comments?post=18418"}],"version-history":[{"count":10,"href":"https:\/\/staging.metax.org\/en\/wp-json\/wp\/v2\/pages\/18418\/revisions"}],"predecessor-version":[{"id":21606,"href":"https:\/\/staging.metax.org\/en\/wp-json\/wp\/v2\/pages\/18418\/revisions\/21606"}],"wp:attachment":[{"href":"https:\/\/staging.metax.org\/en\/wp-json\/wp\/v2\/media?parent=18418"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}